What are the Properties of Acid Alpha Glucosidase?
Acid alpha glucosidase is a lysosomal enzyme with an optimal pH of around 4.5-5.5. It is a glycoprotein with multiple glycosylation sites, which are important for its stability and activity. The enzyme has a high specificity for glycogen and its activity can be measured using synthetic substrates like 4-methylumbelliferyl-α-D-glucopyranoside.